CRANIOFACIAL AND DENTAL MANIFESTATIONS OF CROUZON’S SYNDROME: A Review of Literature and Report of an Illustrative Case :  Craniofacial and Dental manifestations of Crouzon’s Syndrome

I. O. Amole; A. O. Aborisade; M. A. Fusami; A. A. Akinlade

Authors

Dr. I O Amole Department of Oral & Maxillofacial Surgery, Faculty of Dentistry, Bayero University Kano Nigeria /Aminu Kano Teaching Hospital, Kano, Nigeria. Author
Dr. A O Aborisade Department of Oral Diagnostic Sciences, Faculty of Dentistry, Bayero University Kano Nigeria /Aminu Kano Teaching Hospital, Kano, Nigeria, Author
Dr. M A Fusami Department of Oral & Maxillofacial Surgery, Aminu Kano Teaching Hospital, Kano, Nigeria Author
Dr. A A Akinlade Department of Oral & Maxillofacial Surgery, Faculty of Dentistry, Bayero University Kano Nigeria /Aminu Kano Teaching Hospital, Kano, Nigeria. Author

Keywords:

Craniosynostoses, Crouzon syndrome, Literature Review

Abstract

OBJECTIVE: This is a report a case of Crouzon Syndrome in a 5
year-old female and review the literature on the presentation and
management of this rare craniofacial anomaly.
CASE REPORT: A 5-year-old girl presented with complaints of
head swelling and protrusion of the eyes associated with relative
prominence of the lower jaw and decreased growth of the mid face
about 9 months after birth. Based on clinical and radiological
findings, a diagnosis of Crouzon’s syndrome was made.

CONCLUSION: There is a need for the development of a
craniofacial team at this center and other African center in view of
the increasing incidence of this anomaly. The patient in the case
report did not receive any intervention in view of resource
limitation despite her urgent need for intra- cranial decompression.

CRANIOFACIAL AND DENTAL MANIFESTATIONS OF CROUZON’S SYNDROME: A Review of Literature and Report of an Illustrative Case