DENTINOGENESIS IMPERFECTA: A Case Report and Review of Literature

Dentinogenesis Imperfecta

Abstract

BACKGROUND: One of the commonest hereditary disorders of 
dentine formation is dentinogenesis imperfecta (DI). It is inherited 
in an autosomal dominant fashion thus affecting the formation and 
mineralization of dentine, which makes the teeth prone to attrition 
and fracture. Early diagnosis and treatment is recommended to 
prevent or mitigate further deterioration of occlusion and teeth, and 
to improve esthetics.  
 
OBJECTIVE: A report of a case of dentinogenesis imperfecta type 
II who presented on account of sequelae of the dental anomaly, to 
highlight the importance of early diagnosis and treatment of the 
condition. 
 
CASE REPORT: A case report of a 14-year-old female presenting 
with dentinogenesis imperfecta with clinical and radiological 
evidence. There were associated (i) acute apical periodontitis of 
tooth 46, (ii) longitudinal crown root fracture of tooth 36 secondary 
to occlusal trauma. Both teeth were extracted; her 26, 27, 37 and 47 
were billed for stainless steel crown placement and acrylic jacket 
crown for 11, 21, 31 and 41. 
 
CONCLUSION: Early diagnosis and treatment of DI is 
recommended to prevent or intercept deterioration of the teeth and 
occlusion, and thus improve aesthetics. Long term follow-up is 
imperative to prevent developing complications and adjust the 
treatment to the changes in the dentition and occlusion.